The Role Of Nutritional Support In Pediatrics For Hereditary And Multifactorial Connective Tissue Disorders

Authors

  • Lola I. Shaykhova Tashkent State Medical University, Republic of Uzbekistan, Uzbekistan

DOI:

https://doi.org/10.55640/eijmrms-05-10-03

Keywords:

Connective tissue disorders, pediatrics, nutrition, collagen

Abstract

Connective tissue disorders (CTDs) in children represent a heterogeneous group of hereditary and multifactorial diseases that primarily affect the structural integrity and function of collagen, elastin, and the extracellular matrix. These disorders often result in musculoskeletal deformities, vascular fragility, and systemic complications. Nutritional support has emerged as a crucial adjunctive therapy in managing CTDs by enhancing tissue repair, modulating inflammation, and improving overall growth and development. This study reviews current evidence on the role of nutrients—such as proteins, vitamins, minerals, and fatty acids—in the management of pediatric connective tissue disorders, emphasizing the importance of individualized nutritional strategies in improving clinical outcomes and quality of life.

References

Brinckmann, J. (2012). Collagen: Primer in structure, processing and assembly. Springer Science & Business Media.

Chen, W., & Tseng, Y. (2021). Nutrition and connective tissue health in pediatric patients. Journal of Pediatric Nutrition and Metabolism, 14(3), 120–132.

Demmler, J. C., Atkinson, M. D., & Roberts, R. (2019). Nutritional deficiencies in children with connective tissue diseases: A population-based cohort study. Pediatric Rheumatology, 17(1), 24.

Kienitz, T., & Quinkler, M. (2020). The role of vitamin D in autoimmune diseases. Endocrine Connections, 9(1), R1–R12.

Malfait, F., & Francomano, C. (2018). The Ehlers–Danlos syndromes: Advances in diagnosis and management. Nature Reviews Rheumatology, 14(10), 596–612.

Miles, E. A., & Calder, P. C. (2021). Omega-3 fatty acids, inflammation, and immunity—Relevance to human health. Nutrients, 13(2), 468.

Sillence, D. O., & Rimoin, D. L. (2016). Osteogenesis imperfecta: An overview. American Journal of Medical Genetics, 170(1), 3–11.

Valente, K., & Campos, L. M. (2022). Nutritional care in juvenile idiopathic arthritis: From inflammation to growth. Clinical Nutrition in Pediatrics, 41(5), 867–874.

Downloads

Published

2025-10-27

How to Cite

Lola I. Shaykhova. (2025). The Role Of Nutritional Support In Pediatrics For Hereditary And Multifactorial Connective Tissue Disorders. European International Journal of Multidisciplinary Research and Management Studies, 5(10), 21–24. https://doi.org/10.55640/eijmrms-05-10-03